Primary immunodeficiency disorders : a historic and scientific perspective /

Primary Immunodeficiency Disorders: A Historic and Scientific Perspective provides a complete historical context that is crucial for students and researchers concerned with primary immunodeficiency. When researchers have a poor understanding of the way we arrived where we are in research, they can m...

Full description

Bibliographic Details
Corporate Author: ScienceDirect (Online service)
Other Authors: Etzioni, Amos (Editor), Ochs, Hans D. (Editor)
Format: eBook
Language:English
Language Notes:English.
Published: Oxford, England ; Waltham, Massachusetts : Academic Press, 2014.
Subjects:
Online Access:Connect to the full text of this electronic book
Table of Contents:
  • Immunity : from serendipitous observations to science-based speciality
  • The discovery of the T- and B- cell compartments
  • Evolution of the definition of primary immunodeficiencies
  • From immunodeficiency to autoimmunity
  • Immunological tests : from the microscope to whole genome analysis
  • Primary immunodeficiency in the developing countries
  • Jeffrey asked us to "do something"! our journey
  • Finally found : the Ataxia-Telangiectasia gene and its function
  • Wiskott-Aldrich syndrome : from a fatal hematologic disorder to a curable immunodeficiency
  • Neutropenia : more genetic defects than ever expected
  • B cell defects : from X-linked to autosomal recessive agammaglobulinemia
  • The discovery of the familial hemophagocytosis syndromes
  • Chronic granulomatous disease : from a fatal disease to a curable one
  • Severe combined immunodeficiency : from discovery to newborn screening
  • Severe combined immunodeficiency as diseases of defective cytokine signaling
  • The hyper IgM syndromes : a long list of genes and years of discovery
  • Unraveling the complement system and its mechanism of action
  • DiGeorge syndrome : a serendipitous discovery
  • The many faces of the hyper IgE syndrome
  • ADA deficiency : the first described genetic defect causing PID
  • The Leukocyte adhesion deficiency story
  • How common variable immune deficiency has changed over six decades
  • From subcutaneous to intravenous immunoglobulin and back
  • History of hematopoietic stem cell transplantation
  • David's story
  • How primary immunodeficiencies have made gene therapy a reality.