Neurogenetics : methods and protocols /

Bibliographic Details
Other Authors: Potter, Nicholas T.
Format: Book
Language:English
Published: Totowa, N.J. : Humana Press, [2003]
Series:Methods in molecular biology (Clifton, N.J.) ; v. 217.
Subjects:
Table of Contents:
  • Determination of gene dosage: utilization of endogenous and exogenous internal standards
  • Semiquantitative PCR for the detection of exon rearrangements in the parkin gene
  • Detection of FMR1 trinucleotide repeat expansion mutations using southern blot and PCR methodologies
  • Extreme expansion detection in spioncerebellar ataxia type 2 and type 7
  • Repeat expansion detection (RED) and the RED cloning strategy
  • Repeat analysis pooled isolation and detection (RAPID) cloning of microsatellite expansions
  • DIRECT technologies for molecular cloning of genes containing expanded CAG repeats
  • Antibody-based detection of CAG repeat expansion containing genes
  • Detection of trinucleotide repeat containing genes by matrix-assisted laser desorption/ionization (MALDI) mass spectrometry
  • Fluorescence PCR and genescan analysis for the detection of CAG repeat expansions associated with Huntington's disease
  • Molecular detection of galactosemia mutations by PCR-ELISA
  • Denaturing high-performance liquid chromatography and sequence analyses for MECP2 mutations in Rett syndrome
  • Mutiplexed fluorescence analysis for mutations causing Tay-Sachs disease
  • Single-strand conformational polymorphism analysis (SSCP) and sequencing for ion channel gene mutations
  • Pulse field gel electrophoresis for the detection of facioscapulohumeral muscular dystrophy gene rearrangements
  • Denaturing gradient gel electrophoresis (DGGE) for mutation detection in Duchenne muscular dystrophy (DMD)
  • Genetic diagnosis of Charcot-Marie-Tooth disease
  • Analysis of human mitochondrial DNA mutations
  • Detection of mitochondrial DNA mutations associated with Leber Hereditary Neuropathy
  • PCR-based strategies for the diagnosis of Prader-Willi/Angelman syndromes
  • Fluorescence in situ hybridization for identifying the genomic rearrangements associated with three myelinopathies : Charcot-Marie-Tooth disease, hereditary neuropathy with liability to pressure palsies, and Pelizaeus-Merzbacher disease
  • Drosophila models of polyglutamine diseases
  • A comparative gene expression analysis of Emery-Dreifus muscular dystrophy using a cDNA microarray
  • The COS-7 cell in vitro paradigm to study myelin proteolipid protein 1 gene mutations
  • In vitro expression systems for the Huntington protein
  • Heterologous expression of ion channels
  • An assay for characterizing in vitro the kinetics of polyglutamine aggregation
  • Characterization of prion proteins
  • Detection of NF1 mutations utilizing the protein truncation test (PTT)
  • Application of the protein truncation test (PTT) for the detection of tuberosis sclerosis complex type 1 and 2 (TSC1 and TSC2) mutations
  • Development and characterization of antibodies that immunoprecipitate the FMR1 protein
  • Immunological methods for the analysis of protein expression in neuromuscular diseases